Canadian Medical Guide > Diseases > Digestive System Diseases > Pancreatic Diseases > Cystic Fibrosis Terms and Definitions




Cystic Fibrosis

Medical Definition: An inherited disease of exocrine glands, affecting most characteristically the pancreas, respiratory system, and sweat glands, usually beginning in infancy and typified by chronic respiratory infections, pancreatic insufficiency, and susceptibility to heat prostration. Cirrhosis of liver occurring in childhood is common and may produce portal hypertension, splenomegaly, and hypersplenism.
Guide Notes: a specific disease entity: do not use for fibrocystic states of various organs

Cystic Fibrosis Medical Definitions and Terms

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