Canadian Medical Guide > Diseases > Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Infant, Newborn, Diseases > Severe Combined Immunodeficiency Terms and Definitions

Severe Combined Immunodeficiency

Medical Definition:	Group of rare congenital disorders characterized by impairment of both humoral and cell-mediated immunity, leukopenia, and low or absent antibody levels. It is inherited as an X-linked or autosomal recessive defect. About half of the patients with autosomal recessive SCID are deficient in the enzyme adenosine deaminase.
Guide Notes:	immunol defic in newborn inf; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES; DF: note short X ref
Also Called:	Bare Lymphocyte Syndrome
Previously Indexed:	Immunologic Deficiency Syndromes (1974-1991)

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