Canadian Medical Guide > Diseases > Digestive System Diseases > Digestive System Abnormalities > Hirschsprung Disease Terms and Definitions




Hirschsprung Disease

Medical Definition: Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.
Guide Notes: acquired megacolon = MEGACOLON
Also Called: Aganglionosis, Colonic,Aganglionosis, Rectosigmoid Colon
Previously Indexed: Megacolon (1966-1982)

Hirschsprung Disease Medical Definitions and Terms

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